Central nervous system involvement in pediatric hemophagocytic lymphohistiocytosis: A single-center descriptive study of clinical features, neurodiagnostic findings, and outcomes [0.03%]
中枢神经系统在儿童噬血细胞综合征中的作用：一项单中心描述性研究，临床特点、神经诊断发现和预后特征
Manan Nath,Anshul Vagrecha,Annie H Roliz et al.
Manan Nath et al.
Hemophagocytic lymphohistiocytosis (HLH) is a life-threatening hyperimmune condition triggered by the pathological activation of T-cells, natural killer cells, and macrophages leading to a cytokine storm with widespread hyperinflammation af...
Jeremy W Jacobs,Garrett S Booth,Victoria Costa et al.
Jeremy W Jacobs et al.
Factor XIII (FXIII) deficiency is a rare bleeding disorder characterized by unstable hemostatic clots due to defective fibrin cross‑linking. Congenital FXIII deficiency arises from variants in the F13A1 (FXIII-A subunit) or F13B (FXIII-B s...
Ciclosporin as upfront therapy in Subcutaneous Panniculitis-like T-cell Lymphoma with aggressive features and in uncomplicated disease: Two case reports and literature review [0.03%]
环孢素作为浆细胞样T细胞淋巴瘤一线治疗的疗效观察：2例报告及文献复习
Brandon K J Tan,Kiat Hoe Ong,Yong Howe Ho et al.
Brandon K J Tan et al.
Francisco Martins,Guilherme Fontinha,José Magalhães et al.
Francisco Martins et al.
Real-world outcomes in patients with relapsed and refractory multiple myeloma with prior proteasome inhibitor and lenalidomide exposure: A single-center study in Sweden [0.03%]
既往接受过蛋白酶体抑制剂和来那度胺治疗的复发难治多发性骨髓瘤患者的预后因素：瑞典单中心研究
Vincent Luong,Muhammad Kashif,Katarina Uttervall et al.
Vincent Luong et al.
The use of proteasome inhibitors (PI) and immunomodulatory drugs (IMiD) such as lenalidomide (Len) in early lines of therapy in multiple myeloma (MM) has resulted in a high proportion of patients with relapsed or refractory multiple myeloma...
Spleen and Bruton's tyrosine kinase inhibitors for the management of adult immune thrombocytopenia: A systematic review and meta-analysis of randomized controlled trials [0.03%]
成人自身免疫性血小板减少症管理中的脾切除术和泰他西普：随机对照试验的系统评价和meta分析
Akhil D Vatvani,Timotius I Hariyanto,Alejandrina C Ramirez et al.
Akhil D Vatvani et al.
Spleen tyrosine kinase (SYK) and Bruton's tyrosine kinase (BTK) inhibitors have emerged as promising targeted therapies for adult immune thrombocytopenia (ITP). However, a comprehensive synthesis of their benefits compared to placebo has no...
Clonal hematopoiesis at the crossroads of Inflammaging and cardiovascular disease: Mechanistic insights and translational horizons [0.03%]
克隆性血细胞增多症位于炎症衰老和心血管疾病交叉路口：机制见解与转化前景
Soumiya Nadar,Taha K Dohadwala,Nitish Kumaresan et al.
Soumiya Nadar et al.
Clonal Hematopoiesis of indeterminate potential (CHIP) has been increasingly recognised as a risk factor for cardiovascular disease (CVD). Recent epidemiological and experimental studies have linked CHIP as an independent risk factor for my...
Ramadan fasting and hematological disorders: clinical considerations, risks, and management strategies [0.03%]
斋月封斋与血液系统紊乱：临床考虑、风险及管理策略
Abdulrahman Nasiri,Ahmed Alahmadi,Manal Alshammari et al.
Abdulrahman Nasiri et al.
Ramadan fasting induces significant physiological adaptations that can affect patients with hematological disorders. While fasting is generally safe for healthy individuals, reduced hydration and nutritional intake during the 13-18 hour fas...
Skills, attitude and knowledge for early-career hematologists: a pragmatic, scientific framework [0.03%]
实用主义科学框架下的青年血液科医师的职业技能、职业态度和职业知识调查
Mohamad Mohty,Yishan Ye,Rahul Banerjee
Mohamad Mohty
Erdheim-Chester Disease in Adults: 11 Cases from a Canadian Rare Diseases Program [0.03%]
成人 Erdheim-Chester 病的临床特征和治疗反应：加拿大罕见病项目的 11 例报告
Stephanie Quon,Emily Leung,Mark Trinder et al.
Stephanie Quon et al.
Erdheim-Chester disease (ECD) is a rare histiocytic neoplasm with highly variable, multisystem manifestations that present significant diagnostic and therapeutic challenges. This retrospective multicenter case series included 11 adult patie...