Assessing hemorrhagic risk in transthyretin cardiac amyloidosis. The haemorrhagic-embolic conundrum [0.03%]
评估转甲状腺素蛋白心脏淀粉样变性出血风险——出血与栓塞的两难困境
Silvia Vilches
Silvia Vilches
RNA-based full length immunoglobulin light chain sequencing reveals lambda constant domain mutations with potential implications for thermodynamic stability in light chain amyloidosis [0.03%]
基于RNA的免疫球蛋白轻链全长测序发现λ恒定区结构域突变及其潜在的热动力学稳定性意义在轻链淀粉样变性中的作用
Eyad Naser,Sara Oubari,Josefine Jakob et al.
Eyad Naser et al.
Background: Systemic light chain amyloidosis is a protein misfolding disorder characterized by deposition of clonal immunoglobulin light chains in vital organs. To date, little is known about the contribution of light cha...
Transient focal neurological episodes in hereditary transthyretin-related amyloidosis treated with liver transplantation: electroencephalographic insights and clinical features [0.03%]
肝移植治疗遗传性转甲状腺素蛋白相关淀粉样变病的短暂性局灶性神经功能障碍发作：脑电图特征及临床表现
Gonçalo Videira,João Moura,Joel Freitas et al.
Gonçalo Videira et al.
Background: Hereditary transthyretin-related (ATTRv) amyloidosis may involve the central nervous system (CNS) years after liver transplantation, causing transient focal neurological episodes (TFNEs). Their mechanisms and ...
Efficacy of diflunisal for hereditary transthyretin amyloidosis: the Swedish real-world experience [0.03%]
diflunisal治疗遗传性转甲状腺素蛋白淀粉样变性的疗效：瑞典的真实世界经验
John L Berk,Kevin J Carroll,Jorge Mejia Baranda et al.
John L Berk et al.
Background: Diflunisal has been shown to slow the progression of hereditary transthyretin (ATTRv) amyloidosis. We examined the efficacy of diflunisal using data from SveATTR, a longitudinal Swedish registry open for patie...
Proline-rich, polybasic peptides are a structurally distinct class of amyloid-reactive peptides [0.03%]
富含脯氨酸、多碱性肽是一类结构上独特的淀粉样反应性肽
Trevor J Hancock,Manasi Balachandran,Angela Williams et al.
Trevor J Hancock et al.
Background: Systemic amyloidosis is a chronic, devastating illness caused by the build-up of misfolded proteins, leading to abdominothoracic organ dysfunction. Currently approved treatment options focus on preventing furt...
Artificial intelligence-enhanced electrocardiogram findings before and after heart transplantation in cardiac amyloidosis [0.03%]
心脏淀粉样变性患者心移植前后人工智能增强的ECG变化特征分析
Kamal Awad,Juan M Farina,Jose N Nativi Nicolau et al.
Kamal Awad et al.
The prognostic value of red blood cell distribution width in AL amyloidosis [0.03%]
红细胞分布宽度在AL型淀粉样变性疾病中的预后价值
Despina Fotiou,Erasmia Boutakoglou,Konstantinos Giannakas et al.
Despina Fotiou et al.
Evaluation of the yield index of genetic counselling for first-degree relatives of patients with hereditary transthyretin cardiac amyloidosis [0.03%]
评估遗传性转甲状腺素蛋白心脏淀粉样变患者一级亲属的基因咨询收益指数
Bérénice Hébrard,Francois Sauer,Julie Pompougnac et al.
Bérénice Hébrard et al.
Left atrial strain identifies early cardiac involvement in variant transthyretin amyloidosis [0.03%]
左心房应变度可识别变异型转甲状腺素蛋白淀粉样变性早期心脏受累状况
Matteo Serenelli,Elisa Gardini,Stefania Marazia et al.
Matteo Serenelli et al.