Joseph G Borer
Joseph G Borer
A major goal of bladder exstrophy (BE) management is achieving urinary continence, most commonly with surgical bladder neck reconstruction (BNR). This is a report of outcome of BNR after complete primary repair of exstrophy (CPRE). At our i...
Dominic Frimberger
Dominic Frimberger
Epispadias is a rare diagnosis and most commonly described as a part of the bladder exstrophy complex. Epispadias is characterized by failure of the urethral plate to tubularize on the dorsum with the defect ranging from a glandular to a pe...
J Todd Purves
J Todd Purves
Until the 1970s, bladder exstrophy was a frequently fatal birth defect that, at the very least, conferred a shortened life span with devastating consequences for afflicted patients. Beginning with the modern era of surgical management, surv...
Aaron T Wild,Paul D Sponseller,Andrew A Stec et al.
Aaron T Wild et al.
Classic bladder exstrophy (CBE) patients are born with a pubic diastasis that increases steadily with age from a mean value of 4 cm at birth to a mean of 8 cm at age 10, compared with a mean normal width of the pubic symphysis of 0.6 cm at ...
Embryology and bony and pelvic floor anatomy in the bladder exstrophy-epispadias complex [0.03%]
膀胱外翻-尿道上裂复合征的胚胎学及骨盆和泌尿生殖窦解剖学
Andrew A Stec
Andrew A Stec
The exstrophy-epispadias complex is a complex congenital anomaly that, although rare, remains the largest genitourinary birth defect that is surgically correctable. The primary defect in exstrophy is a derangement in midline developmental t...
Cenk S N Buyukunal,John P Gearhart
Cenk S N Buyukunal
The first description of bladder exstrophy was noted on Assyrian tablets nearly 4000 years ago. Since then various papers has been published with an increasing rate. According to the available historical data, almost all operative technique...
Seminars in Pediatric Surgery. The exstrophy-epispadias-cloacal exstrophy spectrum: a new appraisal. Preface [0.03%]
小儿外科研讨会。尿道下裂-尿道上裂-泄殖腔外翻序列征：新的评估。前言
John P Gearhart,Cenk S N Buyukunal
John P Gearhart
Surgery in congenital hyperinsulinism-tips and tricks not only for surgeons. A practical guide [0.03%]
先天性高胰岛素血症外科治疗的经验与技巧——不仅针对外科医生的实用指南
Winfried Barthlen
Winfried Barthlen
Each form of congenital hyperinsulinism (CHI)-focal, diffuse, atypical-requires its own surgical strategy and technique. Focal CHI is treated by a positron emission tomography/computed tomography-guided, local resection which is confined on...
Carmen Capito,Pascale de Lonlay,Virginie Verkarre et al.
Carmen Capito et al.
Beyond the 2 classical forms of congenital hyperinsulinism, focal and diffuse, we report our experience on the surgical treatment of atypical forms. We define 2 subtypes among these atypical forms of hyperinsulinism: in case of a giant foca...
Agostino Pierro,Shireen A Nah
Agostino Pierro
Congenital hyperinsulinism of infancy (CHI) is characterized by inappropriate insulin secretion resulting in persistent hypoglycemia, which can lead to irreversible severe neurological damage in the infant. Many patients with CHI will respo...