The Garbose Family Special Delivery Unit: a new paradigm for maternal-fetal and neonatal care [0.03%]
加尔博斯家庭特殊分娩单元：母胎及新生儿护理新模式
Lori J Howell
Lori J Howell
Birth defects remain the leading cause of infant mortality in the United States according to the Centers for Disease Control. For many anomalies, etiology remains unknown, management and outcome vary widely, and treatment is costly. Great s...
N Scott Adzick
N Scott Adzick
David J Wilkinson,David H Edgar,Simon E Kenny
David J Wilkinson
The current management of Hirschsprung's disease (HSCR) is still associated with significant long-term morbidities despite on-going refinements in surgical care. Over the course of the past 20 years, significant inroads have been made in ou...
Matthew W Ralls,Arnold G Coran,Daniel H Teitelbaum
Matthew W Ralls
Despite most children undergoing a successful pull through for Hirschsprung disease, a small portion of children are left with persistent stooling issues. Most of these stooling issues can be addressed by nonoperative approaches. However, i...
The Hirschsprungs patient who is soiling after what was considered a "successful" pull-through [0.03%]
所谓的“成功”的拉通过后的Hirschsprung患者出现大便失禁
Marc A Levitt,Belinda Dickie,Alberto Peña
Marc A Levitt
After surgery for Hirschsprungs disease, most children thrive, have few if any episodes of abdominal distention and enterocolitis, and are fecally continent. However, there exists a small group of patients who do not do well. Either they su...
Risto J Rintala,Mikko P Pakarinen
Risto J Rintala
Despite significant developments in the understanding of the pathologic anatomy and physiology of Hirschsprung's disease (HD), the results of surgical therapy remain far from perfect. The functional defects and psychosocial difficulties tha...
Philip K Frykman,Scott S Short
Philip K Frykman
Hirschsprung-associated enterocolitis remains the greatest cause of morbidity and mortality in children with Hirschsprung disease. This chapter details the various approaches used to treat and prevent this disease process. This includes pre...
Kelly Miller Austin
Kelly Miller Austin
Hirschsprung's disease-associated enterocolitis (HAEC) remains the most life-threatening complication in Hirschsprung disease (HD) patients. The pathogenesis of HAEC has not been determined and many hypotheses regarding the etiology of HAEC...
Prem Puri,Jan-Hendrik Gosemann
Prem Puri
Variants of Hirschsprung disease are conditions that clinically resemble Hirschsprung disease, despite the presence of ganglion cells in rectal suction biopsies. The characterization and differentiation of various entities are mainly based ...
Samuel W Moore
Samuel W Moore
Total colonic aganglionosis (TCA) is a relatively uncommon form of Hirschsprung disease (HSCR), occurring in approximately 2%-13% of cases. It can probably be classified as TCA (defined as aganglionosis extending from the anus to at least t...