Spyros A Papiris,Maria Kallieri,Maurizio Zompatori et al.
Spyros A Papiris et al.
Autoimmune Pulmonary Alveolar Proteinosis (aPAP) is a rare disease characterized by abnormal accumulation of surfactant in alveoli. Pathogenetically, in aPAP the presence of granulocyte macrophage-colony stimulating factor (GM-CSF) autoanti...
Christen Vagts,Christian Ascoli,Jeffrey R Jacobson
Christen Vagts
Sarcoidosis is a granulomatous disease of unknown cause, triggered by an unidentified antigen. Although classically considered a T cell-mediated disorder with an IFN-γ signature driven by Th1, Th17, and Th17.1 cells, its pathogenesis refle...
M Patricia Rivera,Catherine R Sears
M Patricia Rivera
Pulmonary Alveolar Microlithiasis: A Review of a Rare Disease Through Rarely Discussed Perspectives [0.03%]
肺泡微结石症:罕见病的少见视角下的综述研究
Göksel Altınışık,Nilüfer Yiğit,Nazlı Çetin
Göksel Altınışık
Pulmonary alveolar microlithiasis (PAM) has been well characterized in terms of its description, genetic background, and diagnostic process for decades; however, no effective prevention or treatment has yet been established. PAM is classifi...
Genetics and social determinants of health as drivers of epidemiologic variation in sarcoidosis [0.03%]
遗传因素和社会决定因素在 sarcoidosis 流行病学差异中的驱动作用
John Odackal,Elliott Crouser,Michelle Sharp et al.
John Odackal et al.
Sarcoidosis is a disease with high morbidity that has variable epidemiology based on genetics and sociodemographic factors. The etiology of this variability remains incompletely understood. This narrative review describes how genetics, soci...
John Murray,Shane OBrien,Patrick Mitchell
John Murray
Diffuse Alveolar Hemorrhage (DAH) is a life-threatening clinical syndrome characterized by bleeding from the pulmonary microcirculation into alveolar spaces. It typicially presents with acute respiratory failure, anemia, and diffuse radiolo...
Catia Cilloniz,Juan M Pericàs,José M Miró et al.
Catia Cilloniz et al.
Pulmonary infection is an important cause of hospitalization, morbidity, and mortality in people living with human immunodeficiency virus (PWH) infection, especially in those with significant immunosuppression. Pneumonia, including Pneumocy...
Non-Invasive Ventilation in Immunocompromised Patients with Respiratory Failure [0.03%]
免疫抑制呼吸衰竭患者的无创通气治疗
Valentina Giammatteo,Alessandra Bisanti,Luca Montini et al.
Valentina Giammatteo et al.
Non-invasive ventilation (NIV) is commonly recommended as respiratory support for selected immunocompromised patients with acute respiratory failure (ARF), offering an alternative to tracheal intubation, which historically carried high mort...
Noninfectious Severe Pulmonary Complications in Immunocompromised Critically Ill Patients [0.03%]
免疫缺陷重症患者的非感染性严重肺并发症
Silvia De Rosa,Sergio Lassola,Francesca Gualdi et al.
Silvia De Rosa et al.
Noninfectious pulmonary complications are a significant cause of morbidity and mortality in immunocompromised patients, particularly in those undergoing hematopoietic stem cell transplantation, solid organ transplantation, chemotherapy, or ...
Pulmonary Amyloidosis [0.03%]
肺淀粉样变性
Stefano Levra,Marcel Opitz,Francesco Bonella
Stefano Levra
Amyloidosis is a heterogeneous group of rare diseases characterized by the deposition of misfolded and insoluble proteins in tissues. Lung involvement, airways or parenchyma, is relatively common, but usually mild. Some patients may develop...