Outpatient ATG-free hematopoietic transplantation for aplastic anemia in limited-resource environments offers excellent results: Data from a single LATAM center [0.03%]
在资源有限的环境中，门诊去ATG造血移植治疗再生障碍性贫血效果出色：来自拉丁美洲单中心的数据
José Carlos Jaime-Pérez,Mariana González-Treviño,Andrés Gómez-De León et al.
José Carlos Jaime-Pérez et al.
Objective: To document the results of outpatient hematopoietic stem cell transplantation (HSCT) from the peripheral blood (PB) of sibling donors without anti-thymocyte globulin (ATG) in the conditioning regimen. ...
Marshall A Lichtman
Marshall A Lichtman
The red cell distribution width (RDW) is a standard variable reported in the complete blood count. It has been found to have a consistent relationship to life expectancy in older individuals, prognosis in patients with cardiovascular diseas...
Clinical characteristics, laboratory features and genetic profile of hemoglobin E (HBB:c.79 G > A)/β (nucleotide -28 A > G) (HBB:c.-78 A > G) -thalassemia subjects identified from community- and hospital-recruited cohorts [0.03%]
来自社区和医院队列的血红蛋白E（HBB：c.79G> A）/β（核苷酸-28A>G）（HBB：c.-78A> G）型地中海贫血患者的临床特征，实验室检测结果和基因型特征
Piyatida Chumnumsiriwath,Prissana Charoenporn,Sawichayaporn Jermnim et al.
Piyatida Chumnumsiriwath et al.
Despite several existing laboratory-based studies of hemoglobin (Hb) E (HBB:c.79 G > A)/ β (nucleotide (NT) -28 A > G) (HBB:c.-78 A > G) -thalassemia, no reports have ever provided clinical severity information as well as dependency of blo...
Carmen Jacob,Lakeesha Piyasundara,Maria Bonello et al.
Carmen Jacob et al.
Recent evidence suggests that systemic conditions, particularly those associated with inflammation, can affect erythrocyte deformability in the absence of haematological conditions. In this exploratory study, we investigated the relationshi...
Observational Study
Blood cells, molecules & diseases. 2024 Nov:109:102881. DOI:10.1016/j.bcmd.2024.102881 2024
Clinical utility of relative telomere length analysis in pediatric bone marrow failure [0.03%]
儿科骨髓衰竭相对端粒长度分析的临床应用价值评估研究进展
Shilpa Amatya,Prateek Bhatia,Sudhanshi Raina et al.
Shilpa Amatya et al.
Introduction: Telomere length related studies are limited in pediatric marrow failure cases due to difficulty in establishing population specific age related normograms. Moreover, there is paucity of data related to clini...
Accelerated phase development in a late-onset adolescent Chediak-Higashi syndrome patient caused by compound novel LYST mutations in the setting of SARS-CoV-2 infection [0.03%]
SARS-CoV-2感染诱发晚发型青少年Chediak-Higashi综合征患者加速期进展1例：新发LYST基因复合杂合突变导致
Ping Guo,Xi Wu,Mingkang Yang et al.
Ping Guo et al.
Chediak-Higashi syndrome (CHS) is a rare autosomal recessive genetic disorder characterized by severe immunodeficiency, albinism and coagulation deficiency. Mostly diagnosed in early childhood, this devastating condition is associated with ...
Sickle cell disease in Indian tribal population: Findings of a multi-centre Indian SCD registry [0.03%]
印度部落人群的镰状细胞病：印度SCD登记数据库的多中心研究结果
Yogita Sharma,Deepa Bhat,Parikipandla Sridevi et al.
Yogita Sharma et al.
Background: Sickle cell disease (SCD) registries provide crucial real-world data on demographics, epidemiology, healthcare, patient outcomes, and treatment efficacy. This paper presents findings from the Indian SCD Regist...
Multicenter Study
Blood cells, molecules & diseases. 2024 Nov:109:102873. DOI:10.1016/j.bcmd.2024.102873 2024
Molecular and biochemical evaluation of oxidative effects of cord blood CD34+ MPs on hematopoietic cells [0.03%]
胎盘微粒对造血细胞氧化作用的分子和生化评价
Zoi Katana,Kyriaki Sianidou,Gregory Kaiopoulos et al.
Zoi Katana et al.
A graft source for allogeneic hematopoietic stem cell transplantation is umbilical cord blood, which contains umbilical cord blood mononuclear cells (MNCs and mesenchymal stem cells, both an excellent source of extracellular microparticles ...
Dysmorphic megakaryocytes in TAFRO syndrome: A case series from a single institute [0.03%]
TAFRO综合征中的形态异常巨核细胞：单一机构的病例系列研究
Shohei Maida,Hiromi Nakagawa,Hiroshi Ureshino et al.
Shohei Maida et al.
TAFRO syndrome is a rare systemic inflammatory disorder of unknown etiology characterized by thrombocytopenia, anasarca, fever, reticulin myelofibrosis, renal dysfunction, and organomegaly. The diagnosis of TAFRO syndrome can be challenging...
Diagnosis and management of acquired aplastic anemia in childhood. Guidelines from the Marrow Failure Study Group of the Pediatric Haemato-Oncology Italian Association (AIEOP) [0.03%]
儿童获得性再生障碍性贫血的诊断和治疗。意大利儿科血液肿瘤协会（AIEOP）骨髓衰竭研究组指南
A Guarina,P Farruggia,E Mariani et al.
A Guarina et al.
Acquired aplastic anemia (AA) is a rare heterogeneous disorder characterized by pancytopenia and hypoplastic bone marrow. The incidence is 2-3 per million population per year in the Western world, but 3 times higher in East Asia. Survival i...
Practice Guideline
Blood cells, molecules & diseases. 2024 Sep:108:102860. DOI:10.1016/j.bcmd.2024.102860 2024