Successful glucocorticoid treatment case for IgG4-related long-standing optic neuropathy [0.03%]
IgG4相关性长期视神经病变成功应用糖皮质激素治疗一例
Soma Fukami,Shin-Ichiro Ohmura,Toshitaka Yukishima et al.
Soma Fukami et al.
Immunoglobulin G4-related disease (IgG4-RD) is a systemic rheumatic disease characterized by the infiltration of IgG4-positive plasma cells and swelling or hypertrophic lesions in various organs. IgG4-RD also involves optic lesions, which i...
Systemic sclerosis complicated by azathioprine-induced iatrogenic immunodeficiency-associated lymphoproliferative disorder: A case report [0.03%]
硫唑嘌呤引起的医源性免疫缺陷相关淋巴增生性疾病并发系统硬化症：病例报告
Ryota Okazaki,Genki Inui,Yoshihiro Funaki et al.
Ryota Okazaki et al.
Lymphoproliferative disorders are rare complications in patients with autoimmune diseases who are receiving immunosuppressive therapy. This case report describes a 74-year-old man with diffuse cutaneous systemic sclerosis, anti-RNA polymera...
SAPHO syndrome with bone destruction in the lumbar vertebral endplates: a case report [0.03%]
骶髂关节炎痤疮脓疱病骨肥厚骨髓炎综合征伴腰椎终板骨破坏1例报告
Shiho Nakano,Arata Nakajima,Masato Sonobe et al.
Shiho Nakano et al.
SAPHO syndrome is a rare inflammatory osteoarticular disorder, which includes autoimmune diseases such as pustulotic arthro-osteitis, inflammatory bowel disease-associated spondyloarthritis, and psoriatic arthritis. There are few reports on...
Successful control of recurrent MAS by canakinumab in a Sjogren syndrome patient with homozygous MEFV P369S variants, and review of literatures [0.03%]
MEFV基因P369S纯合突变的原发干燥综合征患者成功应用卡那奴单抗治疗复发性周期性发热-皮肤粘膜炎-血小板减少综合征一例及文献复习
Nobuyuki Ono,Motoki Yoshimura,Toshiya Nishida et al.
Nobuyuki Ono et al.
Macrophage activation syndrome (MAS) is an autoinflammatory condition, which severely complicates autoimmune diseases, such as SJIA, AOSD and SLE. MEFV gene encodes a component of Pyrin inflammasome, whose variants cause familial Mediterran...
Low-density lipoprotein apheresis for refractory lupus nephritis: A case demonstrating marked improvement in proteinuria, hematuria, and renal function [0.03%]
难治性狼疮肾炎低密度脂蛋白血浆吸附治疗病例分享
Narumichi Iwamura,Yuta Matsukuma,Kanako Tsutsumi et al.
Narumichi Iwamura et al.
Systemic lupus erythematosus (SLE) predominantly involves the kidneys, causing lupus nephritis. Patients with diffuse proliferative lupus nephritis frequently experience poor outcomes despite advances in immunosuppressive therapies. Low-den...
Breakthrough herpes zoster following recombinant zoster vaccinations in a rheumatoid arthritis patient receiving a Janus kinase inhibitor: A case report and literature review [0.03%]
接受Janus激酶抑制剂治疗的类风湿关节炎患者在接受重组带状疱疹疫苗后出现突破性带状疱疹一例及文献复习
Shunya Nagata,Naoto Yokogawa
Shunya Nagata
The recombinant zoster vaccine (RZV) is immunologically and clinically effective in immunosuppressed patients. Though rheumatoid arthritis (RA) and the Janus kinase inhibitor (JAKi) increase the risk of herpes zoster (HZ) infection, breakth...
12-Year-Old Girl with Systemic Lupus Erythematosus Complicated by Gangrene and Intermittent Claudication [0.03%]
系统性红斑狼疮合并卒中及间歇性跛行的一例12岁女孩
Takashi Uechi,Tomoko Horinouchi,Yuta Inoki et al.
Takashi Uechi et al.
Systemic lupus erythematosus (SLE) can present with various symptoms, including rare manifestations such as gangrene. This report describes a 12-year-old girl with SLE who presented with intermittent claudication and gangrene. Although inte...
A case of newly onset rheumatoid arthritis successfully treated with methotrexate under the anti-retrovirus therapy against HIV infection [0.03%]
1例人类免疫缺陷病毒感染抗逆转录治期间新发类风湿关节炎患者采用甲氨蝶呤治疗后缓解的病例报告
Ippei Miyagawa,Shingo Nakayamada,Kazuyoshi Saito et al.
Ippei Miyagawa et al.
The patient was a 70-year-old woman. In July 2018, she developed pneumocystis pneumonia and was diagnosed with human immunodeficiency virus (HIV) infection and acquired immunodeficiency syndrome (AIDS). Antiretroviral therapy (ART) was cont...
Granulomatosis with Polyangiitis Initially Presenting as Frequent Urination Mimicking a Prostatic Abscess: A Case Report [0.03%]
以类似前列腺脓肿的尿频为首发症状的肉芽肿性多血管炎1例报告
Riko Kamada,Makoto Hibino,Hikari Higa et al.
Riko Kamada et al.
Granulomatosis with polyangiitis (GPA) rarely involves the urological system. Herein, we report the case of a 71-year-old man with GPA who presented with frequent urination and a computed tomography detected low-density area in the enlarged...
Successful switching treatment of mepolizumab for refractory eosinophilic granulomatosis with polyangiitis and multiple organ dysfunction under benralizumab treatment: A case report [0.03%]
贝那利珠单抗治疗难治性嗜酸性肉芽肿伴聚变性血管炎并多器官功能障碍切换成功使用美泊利单抗的病例报告
Toshitaka Yukishima,Haruka Yonezawa,Yuya Aono et al.
Toshitaka Yukishima et al.
Eosinophilic granulomatosis with polyangiitis (EGPA) is a rare necrotising vasculitis affecting small vessels accompanied by eosinophilic inflammation. Biological therapies, particularly anti-interleukin-5 (IL-5) monoclonal antibodies, have...