Macrophage activation syndrome with hypoplastic marrow and Orbital myositis as a unique initial presentation of Systemic Lupus Erythematosus: A Case-Based Review [0.03%]
低增生骨髓伴发眼眶肌炎作为系统性红斑狼疮的独特初始表现导致的巨噬细胞活化综合征：病例综述
Kaustav Bhowmick,Srijana Pradhan,Uddalok Das et al.
Kaustav Bhowmick et al.
Macrophage activation syndrome (MAS) with hypoplastic marrow is a rare, but life-threatening presenting manifestation of systemic lupus erythematosus (SLE). Lupus orbitopathy also is very rarely reported in the literature. We hereby report ...
The role of syphilis in exacerbating axial spondyloarthritis symptoms: A case report on diagnosis and management [0.03%]
梅毒加重轴向银屑病性关节炎症状的一例报道及诊治体会
Junya Kitai,Takahiro Seno,Naoka Kamio et al.
Junya Kitai et al.
Syphilis, caused by Treponema pallidum, is resurging globally, with diverse clinical manifestations. While musculoskeletal involvement is recognized, its role in exacerbating axial spondyloarthritis (ax-SpA) or causing infectious spondyliti...
Successful treatment by systemic corticosteroids and intravenous cyclophosphamide in acquired pure red cell aplasia associated with systemic lupus erythematosus [0.03%]
系统性红斑狼疮相关获得性纯红细胞再生障碍的治疗体会：1例报道及5例中国患者资料分析
Takafumi Tsushima,Masashi Fukuta,Natsumi Yoda et al.
Takafumi Tsushima et al.
Commonly acquired pure red cell aplasia (PRCA) can be associated with an underlying autoimmune disease. Reports of PRCA associated with systemic lupus erythematosus (SLE) are rare, and no treatment strategies have been documented. We report...
A rare large vessels involvement in a patient with a clinical diagnosis of Granulomatosis with polyangiitis: A case report [0.03%]
肉芽肿性多血管炎临床诊断的1例大血管受累的病例报道
Mona Terkmani,Yasmin Najjar,Fatema Naddaf et al.
Mona Terkmani et al.
A previously healthy 22-year-old female presented with complaints of fatigue, joints pain, headache, fever and night sweats for several months. She also reported a reddish painful left eye and a rash on her legs two months ago. On examinati...
Atypical Lymphoproliferative Disorder and Acquired Angioedema in Systemic Lupus Erythematosus and Sjögren's Syndrome: A Diagnostic Challenge [0.03%]
系统性红斑狼疮和舍格伦综合征中的非典型淋巴增生性疾病与获得性血管神经性水肿：一个诊断难题
Junya Kitai,Takahiro Seno,Masataka Kohno et al.
Junya Kitai et al.
We report a case of a 33-year-old woman presenting with facial erythema, pharyngitis, and progressive cervical lymphadenopathy with tongue, pharyngeal, and laryngeal edema. Laboratory evaluations revealed an elevated soluble interleukin-2 r...
Successful re-administration of tocilizumab in a patient with adult-onset Still's disease after improvement of macrophage activation syndrome [0.03%]
成人斯蒂尔病伴噬血细胞综合征改善后托珠雅玛再次使用成功一例报告
Yuma Nagasawa,Kaoru Takase-Minegishi,Soichiro Adachi et al.
Yuma Nagasawa et al.
Tocilizumab (TCZ) is effective for inducing remission in adult-onset Still's disease (AOSD), but its use may occasionally trigger macrophage activation syndrome (MAS). The rationale for re-introducing TCZ in patients with a history of MAS i...
Neurosarcoidosis or Granulomatosis with polyangiitis? a complex case of a brain mass [0.03%]
神经肉芽肿还是嗜酸性肉芽肿性多血管炎？一例复杂的脑部肿块病例
Luisa Fernanda Jiménez-Arcia,Estiven Crespo-Vizcaíno,Alexandra González-Montoya et al.
Luisa Fernanda Jiménez-Arcia et al.
Sarcoidosis is an immune-mediated systemic disease characterized by the presence of non-caseating granulomas in various parts of the body in the absence of another defined etiology. Neurologic involvement (neurosarcoidosis), which occurs in...
Khalid El-Jack,Fawaz Naeem,Jenelle Safadi et al.
Khalid El-Jack et al.
Giant cell arteritis is a systemic vasculitis that causes inflammation in medium and large-sized blood vessels. The condition can lead to irreversible blindness if not recognized and treated promptly with high-dose steroids. Clinical manife...
Effect of abatacept added to mycophenolate mofetil for refractory calcinosis in juvenile dermatomyositis [0.03%]
阿巴西普联合吗替麦胍酯治疗幼年皮肌炎伴难治性钙质沉着症的疗效
Maho Shimizu,Haruna Nakaseko,Yoshinao Muro et al.
Maho Shimizu et al.
Calcinosis is an intractable condition in juvenile dermatomyositis. The effect of abatacept on calcinosis remains controversial. We describe a case of an 8-year-old boy in whom the addition of abatacept to mycophenolate mofetil was effectiv...
Necrotizing Renal Vasculitis Associated with Sarcoidosis in a Patient with Esophageal Cancer: A Case Report [0.03%]
食道癌患者结节病相关的坏死性肾血管炎的一例报告
Tsuneo Sasai,Ryosuke Hiwa,Shion Kachi et al.
Tsuneo Sasai et al.
Sarcoidosis is a multisystem disorder characterized by non-caseating granulomas, often involving the lungs and lymph nodes, but can affect nearly any organ. Renal involvement in sarcoidosis typically presents as hypercalcemia or interstitia...