A Case of Lipoprotein Glomerulopathy with apoE Chicago and apoE (Glu3Lys) Treated with Fenofibrate [0.03%]
一例以阿波E芝加哥和阿波E(GLU3LYS)表现为脂蛋白肾小球病的病人经非诺贝特治疗后的病例报告
Hitoshi Kodera,Yasuhide Mizutani,Satoshi Sugiyama et al.
Hitoshi Kodera et al.
Lipoprotein glomerulopathy (LPG) is characterized by the accumulation of lipoprotein thrombi within glomerular capillaries. This rare disorder is associated with various types of mutations in the apolipoprotein E gene (apoE). Herein, we pre...
AA Amyloidosis and Atypical Familial Mediterranean Fever with Exon 2 and 3 Mutations [0.03%]
淀粉样变伴 exon 2 和 exon 3 突变的不典型地中海发热综合征病例报告
Junko Yabuuchi,Noriko Hayami,Junichi Hoshino et al.
Junko Yabuuchi et al.
A 54-year-old Japanese man presented with recurrent abdominal pain, fever lasting >5 days, and renal failure. AA amyloidosis was proven by renal and gastric biopsy. Symptoms subsided with the administration of colchicine, but a subsequent r...
Tubuloreticular Inclusions in the Absence of Systemic Lupus Erythematosus and HIV Infection: A Report of Three Pediatric Cases [0.03%]
未患系统性红斑狼疮和HIV感染儿童的管状网状小体包涵结构一例报告
Ayah Elmaghrabi,Elizabeth Brown,Ei Khin et al.
Ayah Elmaghrabi et al.
Tubuloreticular inclusions (TRIs) are subcellular structures located within the cisternae of endoplasmic reticulum. Formation of TRIs has been linked to the exposure of excess interferon (IFN), either from endogenous or exogenous sources. I...
Case Report of Spontaneous Remission of Biopsy-Proven Idiopathic Immune Complex-Mediated Membranoproliferative Glomerulonephritis [0.03%]
一例经肾活检证实的特发性免疫复合物介导的膜增生性肾小球肾炎自发缓解病例报告
Rehan Shah,Mark S Segal,Michael J Wilkowski
Rehan Shah
Membranoproliferative glomerulonephritis (MPGN) is a histopathologic diagnosis causing microscopic hematuria, nephrotic range proteinuria, and chronic renal failure. Current understanding divides pathogenesis into two broad categories: immu...
Florence A Aeschlimann,Rae S M Yeung,Ronald M Laxer et al.
Florence A Aeschlimann et al.
Pulmonary renal syndrome refers to an association of pulmonary and glomerular disease and includes disorders, such as the ANCA-associated vasculitides, anti-glomerular basement membrane antibody disease, systemic lupus erythematosus, and Ig...
Hemodialysis Arteriovenous Access Occlusion Using the Amplatzer Vascular Plug in Patients with Intractable Arm Edema [0.03%]
用于治疗顽固性肢体水肿的血液透析动静脉内瘘阻塞的Amplatz血管栓子封堵术
Michele Di Filippo,Danilo Barbarisi,Doriana Ferrara et al.
Michele Di Filippo et al.
Objectives: Vascular occlusion of hemodialysis arteriovenous access (AVA) using an Amplatzer vascular plug (AVP; St. Jude Medical, St. Paul, MN, USA) is an arising and alternative practice in selected patients; however, f...
Erdheim-Chester Disease Presenting with Secondary Hypertension as a Result of Bilateral, Proximal Renal Artery Stenosis: A Case Report [0.03%]
双侧近端肾动脉狭窄所致二次高血压的 Erdheim-Chester 病1例报告
Farid Arman,Hania Shakeri,Niloofar Nobakht et al.
Farid Arman et al.
Erdheim-Chester disease (ECD) is a rare, non-Langerhans cell histiocytosis presenting most commonly with bone and central nervous system symptoms, including but not limited to bone pain and diabetes insipidus. We present a known case of ECD...
Cisplatin Therapy Does Not Worsen Renal Function in Severe Antenatal Bartter Syndrome [0.03%]
卡托普利治疗不会恶化严重宫内巴特氏综合征的肾功能
Thomas R Welch,David R Shaffer,Darren R Feldman
Thomas R Welch
A 30-year-old man with severe antenatal Bartter syndrome, diagnosed and treated in infancy, developed testicular carcinoma. Despite the known renal complications of cisplatin, this drug was used for his chemotherapy because of its superior ...
Asmaa S Abu Maziad,Jose Torrealba,Mouin G Seikaly et al.
Asmaa S Abu Maziad et al.
Systemic lupus erythematosus (SLE) is an autoimmune disease characterized by development of autoantibodies to nuclear and cytoplasmic antigens. A small subset of SLE patients who had the typical clinical features of SLE was reported to show...
Extracranial Aneurysms in 2 Patients with Autosomal Recessive Polycystic Kidney Disease [0.03%]
两例常染色体隐性多囊肾病患者的颅外动脉瘤
Daniel S Elchediak,Anne Marie Cahill,Emma E Furth et al.
Daniel S Elchediak et al.
Unlike autosomal dominant polycystic kidney disease (ADPKD), autosomal recessive polycystic kidney disease (ARPKD) is not generally known to be associated with vascular abnormalities. Only 4 cases of ARPKD patients with intracranial aneurys...