Renoprotective effects of combination therapy with tolvaptan and dapagliflozin in autosomal dominant polycystic kidney disease: a four-case series [0.03%]
托伐普坦和达格列净联合治疗常染色体显性多囊肾病的肾脏保护作用：系列4例报告
Junji Nishida,Mayuko Yamakawa,Shoko Miura et al.
Junji Nishida et al.
Autosomal dominant polycystic kidney disease (ADPKD), the most prevalent inherited kidney disorder, progresses inexorably to end-stage kidney disease (ESKD) with the vasopressin V2-receptor antagonist tolvaptan serving as a primary treatmen...
Successful treatment of MPO-ANCA positive crescentic IgA nephropathy/IgA vasculitis with nephritis potentially triggered by a COVID-19 vaccine in a young adult female using corticosteroids, rituximab, and avacopan [0.03%]
一名年轻女性患者的特殊病例：新冠肺炎疫苗后环状混合型IgA肾病/ IgA血管炎的治疗经历
Ken Kaseda,Ryou Terakawa,Rena Matsui et al.
Ken Kaseda et al.
An 18-year-old female presented with palpable purpura nine months before her hospital admission, which first appeared 1 month after receiving a COVID-19 vaccine and recurred intermittently. One month prior to admission, she developed macroh...
A case of lupus nephritis with masked polyclonal IgG presenting as severe AKI, successfully treated and withdrawn from hemodialysis: a case report [0.03%]
一例以严重急性肾损伤表现的被多克隆IgG掩蔽的狼疮性肾炎病例报告：治疗成功并脱离透析
Kazuhiro Takeuchi,Kasumi Sato,Hideaki Kuno et al.
Kazuhiro Takeuchi et al.
Lupus nephritis (LN) is well-known as an immune-mediated glomerulonephritis characterized by the full-house pattern of immunoglobulin (Ig) and complement deposition. The "masked IgG" is a recently recognized concept in which IgG appears neg...
Tubular damage and SGLT2 expression in a patient with Beni-koji tablet-associated acute kidney injury and Fanconi syndrome [0.03%]
使用滨子鸡片引起急性肾损伤和范康尼综合征一例的管状损害及SGLT2表达分析
Ayaka Kamada,Takuo Hirose,Hideaki Hashimoto et al.
Ayaka Kamada et al.
Since March 2024, many cases of renal dysfunction have been reported in Japan among individuals taking a supplement containing red yeast rice. We present the case of a 51-year-old woman who developed renal dysfunction and Fanconi syndrome a...
Fumiya Sato,Shingo Nakayama,Takuo Hirose et al.
Fumiya Sato et al.
Minimal change disease (MCD) is a common cause of idiopathic nephrotic syndrome (NS). MCD patients are complicated by acute kidney injury (AKI). Gastrointestinal disorders also occur during the course of NS; however, acute appendicitis afte...
Clinicopathological features of familial fibronectin glomerulopathy caused by a splice site variant in the Fibronectin 1 gene: a case report [0.03%]
纤维蛋白原糖胺聚糖病家系一例临床及病理分析报告
Yoshikuni Nagayama,Masako Otani,Mariko Hashimoto et al.
Yoshikuni Nagayama et al.
Fibronectin glomerulopathy (FNG) is a rare autosomal dominant inherited disease characterized by extensive deposits of fibronectin in the mesangium and subendothelial space of the glomeruli with membranoproliferative glomerulonephritis (MPG...
Human immunodeficiency virus-associated nephropathy mainly due to cellular variant of focal segmental glomerulosclerosis [0.03%]
与人类免疫缺陷病毒相关的肾病主要由于局灶性节段性肾小球硬化细胞变异引起
Hikaru Tanimizu,Naoki Sawa,Akinari Sekine et al.
Hikaru Tanimizu et al.
A 45-year-old man with a low titer of hepatitis B virus (HBV) was diagnosed with nephrotic syndrome. A subsequent test for human immunodeficiency virus (HIV) was positive. Kidney biopsy revealed some signs of collapsing variant of focal seg...
Genetic and protein structure prediction analyses identify a rare pathogenic PKD1 variant causing autosomal dominant polycystic kidney disease [0.03%]
遗传学和蛋白质结构预测分析确定了导致常染色体显性多囊肾病的罕见致病变异PKD1变异体
Takamitsu Shiiya,Hirofumi Watanabe,Ryo Aida et al.
Takamitsu Shiiya et al.
Autosomal dominant polycystic kidney disease (ADPKD) is one of the most common monogenic kidney disorders. The diagnosis of ADPKD requires imaging findings showing multiple kidney cysts or genetic testing, in cases where a family history is...
A case of systemic contact dermatitis associated with a peritoneal dialysis catheter and treated with dupilumab [0.03%]
与腹膜透析导管有关并用Dupilumab治疗的一例系统接触性皮炎
Kosuke Mochizuki,Jun Takeoka,Naohiro Toda et al.
Kosuke Mochizuki et al.
Eosinophilia during the induction of peritoneal dialysis (PD) is frequently caused by icodextrin, but allergic reactions to PD catheters have been rarely reported. In previous reports, PD catheter-induced systemic contact dermatitis in pati...
Systemic AA amyloidosis with amyloid deposition in the peritoneum at the time of initiating peritoneal dialysis [0.03%]
腹膜透析起始时合并腹膜内淀粉样变性的系统性AA淀粉样变性病一例报告
Masato Habuka,Chihiro Sakurazawa,Yuichi Sakamaki et al.
Masato Habuka et al.
Amyloidosis is characterized by the deposition of insoluble amyloid fibrils formed by disease-specific precursor proteins in the extracellular interstitium of various organs throughout the body, resulting in organ damage. Patients with amyl...