Treatment decision-making for using CFTR modulator therapy in patients with cystic fibrosis [0.03%]
囊性纤维化患者使用CFTR调控剂治疗的决策问题
Alison Carr,Carlos Carneiro,Michael Griffin et al.
Alison Carr et al.
Background: Five cystic fibrosis transmembrane conductance regulator (CFTR) modulator (CFTRm) therapies are approved for patients with cystic fibrosis (CF). Despite the established efficacy and safety of CFTRm therapy, va...
Cancer screening & beyond: The increasing need for primary care in cystic fibrosis [0.03%]
肺癌筛查及以后：囊性纤维化患者对初级保健需求的增加
Karina Z Whelan,A Whitney Brown
Karina Z Whelan
Validation of the CFAbd-Score.kid©, a Novel gastrointestinal patient reported outcome measure, specific for children with cystic fibrosis [0.03%]
CFAbd-Score.kid©有效性验证，该量表是一种针对囊性纤维化患儿的新型胃肠道患者报告结局测评工具
Pauline Sadrieh,Lilith Bechinger,Franziska Duckstein et al.
Pauline Sadrieh et al.
Background: Abdominal symptoms (AS) relevantly impair quality of life (QoL) in people with Cystic fibrosis (CF). Following FDA guidelines, we previously developed and validated the CFAbd-Score©, the first CF-specific gas...
Nicolas Henao-Romero,Lingxiu Susan Liu,Amirala O M Nazari et al.
Nicolas Henao-Romero et al.
Background: Gastrointestinal (GI) complications are a common source of morbidity for people with cystic fibrosis (pwCF). The pathobiology of these clinical presentations is not fully understood, but there is evidence that...
The changing face of cystic fibrosis research: challenges of multi-centre microbiology cohort studies [0.03%]
支气管扩张症多中心微生物组队列研究的挑战
Ieuan Es Evans,Christine M Duplancic,Timothy A Kidd et al.
Ieuan Es Evans et al.
Introduction: Infection is a primary cause of progressive pulmonary disease in people with cystic fibrosis (pwCF). Researchers frequently utilize data registries or centre-based cohort studies to study infections in CF. W...
After the earthquake: Unmet needs in people with cystic fibrosis in Turkiye- multicenter study [0.03%]
地震后土耳其囊性纤维化患者未满足的需求-多中心研究
Seyda Karabulut,Velat Sen,Beste Özsezen et al.
Seyda Karabulut et al.
Background: We aimed to assess unmet needs of pwCF in the earthquake zone by income level. Methods: Following the February 6, 2023 Eart...
Bone mineral density in children and adolescents with cystic fibrosis: a longitudinal study [0.03%]
囊性纤维化患儿及青少年骨密度的纵向研究
G Tamer,H M van Santen,Hgm Arets et al.
G Tamer et al.
Background: Adults with cystic fibrosis (CF) show a higher rate of osteoporosis compared to healthy adults. Achieving proper adult bone mass is a process starting in childhood. We aimed to evaluate the prevalence, course ...
Dietary intakes and quality of Irish adults with cystic fibrosis: Comparisons to nutrition guidelines and HEI-2020 [0.03%]
爱尔兰囊性纤维化成人患者的膳食摄入与质量及其与营养指南和HEI-2020的比较
Cian Greaney,Ellen McCarthy,Lauren O&#x;Brien et al.
Cian Greaney et al.
Background: With evolving Cystic Fibrosis (CF) phenotypes resulting from changes to clinical management, healthier dietary practices are warranted for many people with CF. Whilst diet composition is reported, diet quality...
Symptom factors and their clinical correlates among adults with cystic fibrosis [0.03%]
囊性纤维化成人患者的症状因素及其临床相关性
Natalia Smirnova,Scott Gillespie,Jane Lowers et al.
Natalia Smirnova et al.
Background: Despite cystic fibrosis transmembrane conductance (CFTR) modulator therapy that may dramatically alter the course of disease, many people living with cystic fibrosis (PwCF) experience co-occurring symptoms tha...
Isolated hyperphosphatasemia in adults with cystic fibrosis - a case series [0.03%]
成人囊性纤维化患者孤立性高磷酸酶血症的病例系列研究
Blair Lenhan,Katie Kaput,HollyAnn Jacobs et al.
Blair Lenhan et al.