The clinical features and outcome of Kawasaki disease combined with G6PD deficiency [0.03%]
G-6-PD缺乏症合并川崎病的临床特征及转归
Peisi Cheng,Tingyan He,Jun Yang
Peisi Cheng
Novel HCK-associated mutation causing autoinflammatory disorder with pulmonary manifestations in a pediatric patient [0.03%]
儿科患者HCK相关新突变导致具有肺部表现的自身炎症性疾病
Afig Berdeli,Shams Ismayilova,Nida Gürbüz
Afig Berdeli
Autoinflammatory diseases, characterized by recurrent systemic inflammation due to innate immune dysregulation, often present with fever, arthritis, abdominal pain, and cutaneous involvement, with elevated acute-phase reactants during flare...
Anakinra for infants under six months with Kawasaki disease and coronary artery lesions: a multicenter case series and literature review [0.03%]
安卡利珠单抗治疗6月龄以下冠状动脉病变型川崎病患儿的多中心病例系列研究及文献回顾
Giulia Inguscio,Stefano Romano,Marianna Fabi et al.
Giulia Inguscio et al.
Background: Infants with Kawasaki Disease (KD) have a higher risk of incomplete presentations, IVIG resistance, and coronary artery lesions (CALs). IL-1 plays a key role in the pathogenesis, highlighting its potential as ...
Vaccination coverage, immune responses, and clinical characteristics in children with PFAPA syndrome: a monocentric prospective study [0.03%]
PFAPA综合征儿童的疫苗接种率、免疫反应及临床特征:单中心前瞻性研究
Emilie Sallansonnet,Renato Gualtieri,Henri Margot et al.
Emilie Sallansonnet et al.
Neutrophil lymphocyte ratio as a marker of skin disease activity in older children with juvenile dermatomyositis [0.03%]
中性粒细胞淋巴细胞比值可作为大龄儿童皮肌炎皮肤活动性的标志
Shreya Swaminathan,Nidhi Naik,Susan Shenoi et al.
Shreya Swaminathan et al.
Background: Neutrophils contribute to the pathogenesis of many autoimmune diseases. While the neutrophil to lymphocyte ratio (NLR) is associated with disease activity in adult dermatomyositis, its clinical utility in juve...
Comparison of clinical practices during the transitional and young adult phases between patients with oligoarticular/polyarticular juvenile idiopathic arthritis and those with rheumatoid arthritis in Japan [0.03%]
日本少关节炎/多关节炎型幼年特发性关节炎与类风湿关节炎患者在过渡期和成年早期的临床实践比较研究
Sho Mori,Kosuke Shabana,Toshihiro Matsui et al.
Sho Mori et al.
Background: Juvenile idiopathic arthritis (JIA) is a chronic inflammatory condition that frequently persists into adulthood, posing long-term challenges in disease control and quality of life. However, clinical management...
Comparative Study
Pediatric rheumatology online journal. 2025 Nov 24;23(1):120. DOI:10.1186/s12969-025-01164-6 2025
Presence and reactivities of antibodies directed to citrullinated peptides in a Swedish JIA cohort [0.03%]
瑞典JIA队列中抗瓜氨酸肽抗体的存在和反应性
Raya Saleh,Erik Sundberg,Monika Hansson et al.
Raya Saleh et al.
Evaluation of the real-world safety of Canakinumab in the treatment of systemic juvenile idiopathic arthritis in children aged 0-16: a comprehensive analysis based on FAERS data [0.03%]
基于FAERS数据库评价卡那奴单抗治疗儿童(0~16岁)系统性 juvenilesidiopathicarthritis安全性的真实世界研究综合分析
Peng Xiao,Bingqi Wei,Guilong Zhang et al.
Peng Xiao et al.
Background: Canakinumab is a fully human monoclonal antibody that primarily targets interleukin-1β (IL-1β) and is primarily indicated for systemic juvenile idiopathic arthritis (sJIA). Since it is predominantly used in ...
Analysis of genes involved in immune response in children with HLH - case series [0.03%]
儿童噬血细胞性淋巴组织细胞增多症相关免疫反应基因分析及病例系列报道
Ewelina Gowin,Witold Szaflarski,Danuta Januszkiewicz-Lewandowska
Ewelina Gowin
Background: Hemophagocytic lymphohistiocytosis (HLH) is an excessive immune activation syndrome. The genetic studies on every patient diagnosed with HLH recently became a standard of care. The likelihood of identifying a ...
Association of Mediterranean diet adherence with familial Mediterranean fever severity in a Lebanese cohort [0.03%]
地中海饮食依从性与黎巴嫩遗传队列中家族性地中海热严重程度的关联
Razane Hammoud,Remie El Helou,Dalal Sabbagh et al.
Razane Hammoud et al.
Background: Familial Mediterranean Fever (FMF) is an autoinflammatory disease characterized by a wide clinical variability among individuals, indicating that both genetic and environmental factors influence disease progre...