Tomasz Rawo,Marek Tramś,Paweł Michalski et al.
Tomasz Rawo et al.
Postural disturbances may cause the worsening of cardiopulmonary function in cystic fibrosis children and adolescents, as well as adversely affect their somatic and psychological development. ...
Dietary pattern and its relationship between bone mineral density in girls and boys with cystic fibrosis - preliminary report [0.03%]
饮食模式及其与囊性纤维化女童和男童骨矿物密度的关系-初步报告
Dorota Sands,Monika Mielus,Wioleta Umławska et al.
Dorota Sands et al.
Background: Nutrition influence on cystic fibrosis (CF) patients survival is well documented and dietary therapy is one of basic elements of their treatment. Prolonged survival of CF patients might yet emerge comorbiditie...
Renal assessment in teenage patients with cystic fibrosis - preliminary report [0.03%]
囊性纤维化青少年患者的肾功能评估-初步报告
Dorota Sands,Joanna Jaworska,Agnieszka Urzykowska et al.
Dorota Sands et al.
Background: Together with increasing life expectancy of patients with cystic fibrosis *CF*, there is a growing need to deal with unforeseen problems and complications. Among others renal dysfunction has become of great co...
Does the mutation of the SERPINA1 gene contribute to liver damage and cholestasis in patients with diagnosed cystic fibrosis? preliminary study [0.03%]
SERPINA1基因的突变是否会导致已被确诊为囊性纤维化的患者的肝损伤和胆汁郁积？初步研究
Sabina Więcek,Halina Woś,Bożena Kordys-Darmolińska et al.
Sabina Więcek et al.
Mutation of the SERPINA1 gene is present in about 2% of patients with cystic fibrosis but is more common and accounts for about 5% in patients with cystic fibrosis and co-existing liver lesions. The SERPINA1 gene is responsible for the synt...
The course of glucose intolerance in children with cystic fibrosis: a retrospective study - preliminary report [0.03%]
囊性纤维化患儿葡萄糖耐受不良的进程：一项回顾性研究-初步报告
Katarzyna Piechowiak,Hanna Trippenbach-Dulska,Katarzyna Walicka-Serzysko
Katarzyna Piechowiak
Diabetes is a common and severe complication of cystic fibrosis. If unrecognized, the condition not only causes deterioration of pulmonary function and failure to gain weight, but also a six-fold increase in mortality. ...
The clinical presentations of pulmonary aspergillosis in children with cystic fibrosis - preliminary report [0.03%]
囊性纤维化儿童肺曲霉病的临床表现-初步报告
Katarzyna Walicka-Serzysko,Dorota Sands
Katarzyna Walicka-Serzysko
Pulmonary aspergillosis is a very serious complication in cystic fibrosis (CF) patients due to the great variety of its clinical presentations and the fact that it worsens the prognosis. We can distinguish the following: Aspergillus coloniz...
Cross-infections with Pseudomonas aeruginosa in patients with cystic fibrosis attending the Warsaw Centre [0.03%]
在华沙中心接受治疗的囊性纤维化患者中的绿脓杆菌交叉感染
Justyna Milczewska,Tomasz Wołkowicz,Katarzyna Zacharczuk et al.
Justyna Milczewska et al.
Aim: 1. To assess the prevalence of cross-infections with P. aeruginosa in order to evaluate the epidemiological situation of this infection in patients with cystic fibrosis attending our centre; 2. To correlate the clini...
Application of positive expiratory pressure *PEP* in cystic fibrosis patient inhalations [0.03%]
正预期呼气压力(PEP)在囊性纤维化患者吸药中的应用
Teresa Orlik,Dorota Sands
Teresa Orlik
Inhalations, whose aim is the liquefaction of dense viscous secretions and preparing them for evacuation from the bronchial tree by means of drainage techniques, are standard treatment procedures in cystic fibrosis. Numerous studies showed ...
Controlled Clinical Trial
Developmental period medicine. 2015 Jan-Mar;19(1):50-9. DOI: 2015
Clinical status and somatic development of patients with or without meconium ileus diagnosed through neonatal screening for cystic fibrosis [0.03%]
通过新生儿囊性纤维化的筛查来诊断是否患有胎便性肠梗阻的患者的临床状态和体格发育情况
Katarzyna Zybert,Ewa Mierzejewska,Dorota Sands
Katarzyna Zybert
The aim of the study was to compare the patients with abnormal result of newborn screening for cystic fibrosis (CF NBS), with or without meconium ileus (MI), in regard to their clinical status at the diagnosis and early childhood somatic de...
Comparative Study
Developmental period medicine. 2015 Jan-Mar;19(1):41-9. DOI: 2015
Meconium ileus in newborns with cystic fibrosis - results of treatment in the group of patients operated on in the years 2000-2014 [0.03%]
2000-2014年间手术治疗的囊性纤维化新生儿胎便粘稠症的结果
Maria Boczar,Ewa Sawicka,Katarzyna Zybert
Maria Boczar
Aim: Evaluation of diagnostic and treatment procedures in children with cystic fibrosis (CF) operated on because of meconium ileus (MI). Material and meth...