Morphological Variations in Haemophilic Knee Arthropathy: Surgical Implications for Total Knee Arthroplasty Component Selection and Bone Preparation [0.03%]
血友病性膝关节炎的形态学变化:全膝关节置换假体选择及骨床准备的外科意义
Seyed Mohammad Javad Mortazavi,Babak Haghpanah,Mohammadreza Razzaghof et al.
Seyed Mohammad Javad Mortazavi et al.
Aim: Knee arthropathy affects 90% of patients with severe haemophilia, with unique morphological changes making TKA technically challenging. We evaluated morphological features of haemophilic knees compared to osteoarthri...
A Comprehensive Approach: Addressing Psychological Needs in Gene Therapy for Haemophilia [0.03%]
全面关怀:基因治疗在血友病患者心理需求中的应用探讨
Aida Peyvandi,Ilaria Cutica,Isabella Garagiola et al.
Aida Peyvandi et al.
Introduction: Gene therapy (GT) represents a transformative development in the treatment of haemophilia, offering the potential for long-lasting symptom control after a single administration. Although the scientific and m...
Safety and Effectiveness of Emicizumab in People With Haemophilia A Enrolled in the ATHN 7 Haemophilia Natural History Study [0.03%]
在ATHN 7血友病自然史研究中注册的血友病A患者的艾美赛珠单抗的安全性和有效性研究
Tyler W Buckner,Shannon L Carpenter,Nabil Daoud et al.
Tyler W Buckner et al.
Background: The Natural History Study of the Safety, Effectiveness, and Practice of Treatment for People with Haemophilia (ATHN 7) monitors use of contemporary haemophilia therapies, including emicizumab, a bispecific ant...
Safety, Efficacy and Treatment Patterns of rIX-FP in Previously Untreated Paediatric Haemophilia B Patients: A Retrospective Chart Review in Japan [0.03%]
日本既往未治疗的儿科B型血友病患者中rIX-FP的安全性、有效性和治疗模式:回顾性图表审核
Keiji Nogami,Chiai Nagae,Masatoshi Yono et al.
Keiji Nogami et al.
Background: Limited real-world data exist on recombinant fusion protein-linking coagulation factor IX (FIX) with albumin (rIX-FP) in paediatric previously untreated patients (PUPs) with haemophilia B, particularly in infa...
Acquired Bleeding Disorders Associated With Immune Checkpoint Inhibitors: An Update [0.03%]
免疫检查点抑制剂相关获得性出血病的更新研究
Marco Tuccori,Daniele Focosi,Elena Arzenton et al.
Marco Tuccori et al.
The Laboratory Monitoring of Altuvoct (Efanesoctocog Alfa): Recommendations From the Laboratory Working Party of the United Kingdom Haemophilia Centres Doctor's Organisation [0.03%]
阿卢福乔特(艾法内索科格艾尔法)的实验室监测:英国血友病中心医生组织实验室工作组的建议
Annette Elizabeth Bowyer,Mohammed Khan,Caroline Lawrence et al.
Annette Elizabeth Bowyer et al.
General recommendations: As assays tailored to Altuvoct are necessary, it is essential that every request for a FVIII level for monitoring of Altuvoct clearly identifies when it has been used for treatment of the patient ...
Cost Analysis of Radioactive Versus Arthroscopic Synovectomy in Haemophilia: A Brazilian Modelling Approach [0.03%]
巴西血友病患者放射性与关节镜下滑膜切除术的成本分析模型方法研究
Sylvia Thomas,Mariana Battazza,Vinicius Bednarczuk de Oliveira et al.
Sylvia Thomas et al.
Introduction: Radioactive synovectomy (RSO) is an alternative to arthroscopic synovectomy (AR), for treating synovitis. RSO reduces the number of hemarthroses, being less invasive and less costly. ...
Validating the Online Self-Administered Bleeding Assessment Tool (Self-BAT) as a Screening Tool for Bleeding Disorders [0.03%]
出血评估工具(Self-BAT)的验证:筛查出血性疾病的新型工具
Veronica DeYoung,Julie Grabell,Wilma Hopman et al.
Veronica DeYoung et al.
Competence and Confidence: An Evaluation of Physiotherapists' Knowledge and Self-Perception About Physical Activity and Exercise in Patients With Haemophilia [0.03%]
能力与信心:关于物理治疗师在血友病患者身体活动和运动方面的知识和自我感知的评估
Ozge Ozkutlu,Melda Comert,Seda Bicici Ulusahin et al.
Ozge Ozkutlu et al.
Introduction: Physiotherapists are irreplaceable in providing safe, tailored physical activity (PA) and exercise in patients with haemophilia (PwH). Aim: ...
Elucidating the Molecular Basis in a Cohort of Patients With Combined Bleeding Tendencies and Joint Hypermobility Manifestations [0.03%]
阐明具有联合出血倾向和关节过度伸展表现患者队列的分子基础
Perla Bandini,Nina Borràs,Carme Altisent et al.
Perla Bandini et al.
Background: In patients with unexplained bleeding and normal haemostatic parameters, heritable disorders of connective tissue (HDCT) may be an underlying cause due to vascular fragility, as observed in Ehlers-Danlos syndr...