Five-Year Experience of Haemophilia Centre Certification Performed by the German, Austrian and Swiss Society for Thrombosis and Haemostasis Research [0.03%]
德国、奥地利和瑞士血栓与止血研究学会进行的血友病中心认证五年经验总结
Hermann Eichler,Hagen Bönigk,Susan Halimeh et al.
Hermann Eichler et al.
Introduction: To enhance the treatment quality in haemophilia centres (HC), the German, Austrian and Swiss Society for Thrombosis and Haemostasis Research (GTH) started in 2017 the development of guidelines to define the ...
Inhibition of CIRBP as a Novel Strategy to Alleviate Chondrocyte Ferroptosis in Haemophilic Arthropathy [0.03%]
抑制CIRBP作为缓解血友病关节炎软骨细胞铁死亡的新策略
Yi Wang,Yi Hu,Fudong Luo et al.
Yi Wang et al.
Background: Haemophilic arthropathy (HA) is a frequent complication of haemophilia, where ferroptosis in chondrocytes significantly contributes to disease progression. Cold-inducible RNA-binding protein (CIRBP) is known t...
Approaches to Identify People With Haemophilia With Medicare Claims Data [0.03%]
利用医疗保险理赔数据识别血友病患者的方法
Stacey A Fedewa,Tyler W Buckner,Lorraine Cafuir et al.
Stacey A Fedewa et al.
Objectives: Medical claims are increasingly used to study haemophilia, a rare and costly X-linked congenital bleeding disorder. However, there is no standard method to identify people with haemophilia A (PwHA) in medical ...
Factor V Levels Required for Perioperative Management of Bleeding in Combined Deficiency of Factors V and VIII [0.03%]
V因子水平在V和VIII因子联合缺乏的手术期出血管理中的指导意义
Elena Yakovleva,Kirill Sabirov,Bin Zhang
Elena Yakovleva
Riitta Lassila,Ferdows Atiq,Caterina Casari et al.
Riitta Lassila et al.
In recent decades the advances in care and therapeutic options for people with haemophilia have been extraordinary, transforming the lives of those with severe disease and access to treatment. In contrast, the treatments for those living wi...
International Practices in Managing Preconception, Pregnancy and Childbirth in Women With Glanzmann Thrombasthenia: A Survey From the European Association of Haemophilia and Allied Disorders (EAHAD) [0.03%]
关于血小板功能障碍性疾病格伦扎姆氏血小板病孕产期管理的国际调查——来自欧洲罕见出血疾病协会的一项调查研究
Karlijn H G Rutten,Roger E G Schutgens,Roseline d&#x;Oiron et al.
Karlijn H G Rutten et al.
Background: Glanzmann thrombasthenia (GT) is an inherited platelet disorder resulting in severely reduced platelet aggregation and increased bleeding tendency. Pregnancy and childbirth in women with GT present significant...
A Novel Heterozygous Mutation in FGB (c.1231_1232 del GA) Causing Hypofibrinogenemia With Mild Bleeding in a Large Swiss family [0.03%]
于一个大家系中发现的导致轻度出血的异染色体新型FGB基因(c.1231_1232delGA)变异导致低纤维蛋白原血症
Sophie Voruz,Jasmine Noetzli,Mathilde Gavillet et al.
Sophie Voruz et al.
Acceptability and Determinants for Implementation of the EnzySystem, a Novel Near-Patient Testing Platform for Haemophilia A [0.03%]
安佳系统(Acceptability和实施决定因素用于A型血友病的近患者检测平台)
Aernoud P Bavinck,Kyle Davis,Lisa van Engelshoven et al.
Aernoud P Bavinck et al.
Introduction: Coagulation testing in haemophilia A is limited by the scarcity of testing facilities capable of performing relevant assays. This issue incentivized the development of the EnzySystem for haemophilia A, a nea...
Integration of Efanesoctocog Alfa in Clinical Practice for Children, Adolescents, and Young Adults With Severe Haemophilia A [0.03%]
艾尼索octocog alfa在儿童、青少年及年轻成人严重甲型血友病患者中的临床应用整合
Debbie Jiang,Natalie Johnston,Daniel Echelman et al.
Debbie Jiang et al.
Introduction: Efanesoctocog alfa is a novel, "ultra-extended half-life" FVIII concentrate for bleed treatment and prevention in haemophilia A. Clinical trials excluded individuals with active or prior FVIII inhibitors, th...
Haemostatic Prophylaxis and Colonoscopy Outcomes in Patients With Bleeding Disorders: An Update [0.03%]
出血性疾病患者的止血预防和结肠镜检查结果：最新进展
Guneet S Janda,Jee Won Shin,Aneel A Ashrani et al.
Guneet S Janda et al.