Smartphone-Based Teledentistry to Support Clinical Triage and Risk-Informed Dental Care in Patients With Inherited Bleeding and Haemoglobin Disorders: A Cross-Sectional Diagnostic Agreement Study [0.03%]
基于智能手机的牙科远程医疗支持临床分诊及血液病和血红蛋白病患者的循证牙科治疗：诊断一致性横断面研究
Victor Cordeiro da Silva,Carolina Mendes Frusca do Monte,Leandro Tavares da Silva et al.
Victor Cordeiro da Silva et al.
Introduction: Patients with inherited bleeding and haemoglobin disorders face barriers to accessing timely dental care, increasing the risk of untreated oral disease and complications related to invasive procedures. ...
Haemophilia Management in Natural Disasters-From Field to Consensus Report [0.03%]
从现场到共识报告：血友病自然灾害管理
Ahmet Muzaffer Demir,Selin Aytaç,Serap Karaman et al.
Ahmet Muzaffer Demir et al.
Objective: The earthquake in Türkiye had a profound impact on both haemophilia patients and healthcare services in the region. This experience highlighted the need for an effective action plan for patients with bleeding ...
Preimplantation Genetic Testing for Families at Risk of Haemophilia: Ten-Year Single-Centre Experience [0.03%]
血友病高风险家庭的植入前遗传学检测：单中心十年经验回顾
Mimosa Mortarino,Isabella Garagiola,Valeria Nicotra et al.
Mimosa Mortarino et al.
Introduction: Preimplantation genetic testing for monogenic diseases (PGT-M) is a reproductive option for couples at high risk of transmitting inherited disorders. We report a ten-year single-centre PGT-M experience in fa...
Real-World Outcomes of Prophylaxis With rIX-FP in Germany: A Prospective, Non-Interventional Study in Haemophilia B [0.03%]
德国使用rIX-FP预防治疗的研究：血友病B患者的前瞻性、非干预性研究
Johannes Oldenburg,Swee Wenning,Susanne Holzhauer et al.
Johannes Oldenburg et al.
Introduction: Efficacy and safety of albutrepenonacog alfa (rIX-FP) in people with haemophilia B (PwHB) has been previously demonstrated in clinical trials. However, real-world data insights are required. ...
Prophylactic Factor Replacement Versus on-Demand Factor Replacement Following Primary Total Knee Arthroplasty in Patients With Hemophilia: A Retrospective Study With an Average 10-Year Follow-up [0.03%]
一项平均随访期长达十年的回顾性研究：血友病患者初次全膝关节置换术后实施预防性凝血因子替代疗法与按需治疗的效果比较
Zhongyu Luo,Xiaoying Zhong,Chen Zhang et al.
Zhongyu Luo et al.
Background: The long-term benefits of prophylactic factor replacement following total knee arthroplasty in patients with hemophilia remain insufficiently evaluated. ...
Accuracy of Factor VIII Assays for Measuring Damoctocog Alfa Pegol: A Comparative Analysis [0.03%]
关于因子VIII检测方法测定达 octocog alfa pegol准确性的比较分析
Judith C A Cluitmans,Piet Meijer,Sanna R Rijpma et al.
Judith C A Cluitmans et al.
Introduction: Accurate monitoring of treatment with modified factor VIII products remains challenging, due to known variability in assay performance across different laboratory methods and reagents. For the extended half-...
Real-World Assessment of rVIII-SingleChain for Prophylactic Treatment in People With Severe Hemophilia A in High-Resource Settings [0.03%]
重度甲型血友病患者预防治疗的单链重组第八因子疗效的真实世界研究
Te-Fu Weng,Shu-Huey Chen,Yeu-Chin Chen
Te-Fu Weng
Introduction: rVIII-SingleChain has been approved and reimbursed in Taiwan since September 2020 as prophylaxis for severe hemophilia A. Aim: ...
Platelet Hyperreactivity May Contribute to Thrombotic Complications in Afibrinogenemia: A Case-Based Observation [0.03%]
基于病例的观察：纤维蛋白原缺乏症患者血小板高反应性可能促使其血栓并发症发生
Liqin Ling,Chaonan Liu,Qianyuan Luo et al.
Liqin Ling et al.
Predictors and Clinical Impact of Time to Diagnosis in Acquired Haemophilia A: An 11-Year Retrospective Cohort Study [0.03%]
获得性血友病A的诊断时间预测因素及其临床影响：一项11年的回顾队列研究
Jing Yuan Tan,Wan Hui Wong,Chi Kiat Yeo et al.
Jing Yuan Tan et al.
Clinical Outcomes of Efanesoctocog Alfa Prophylaxis in Children With Severe Haemophilia A: Interim Data From XTEND-ed [0.03%]
艾尼索科格α型 prophylactic治疗严重甲型血友病儿童的临床结局：XTEND-ed中期数据分析
Lynn Malec,Beatrice Nolan,Anthony K C Chan et al.
Lynn Malec et al.