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Pulmonary Artery Denervation for Refractory Sjögren's Syndrome-Associated Pulmonary Arterial Hypertension: A Case Report of Combined Hemodynamic and Renal Recovery

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A 31-year-old woman with primary Sjögren's syndrome presented with severe pre-capillary pulmonary arterial hypertension (mean pulmonary arterial pressure 51 mmHg, pulmonary vascular resistance 14.7 Wood units) and active renal impairment (24-hour urinary pro... ...