Transapical beating-heart septal myectomy for Fabry cardiomyopathy with left ventricular outflow tract obstruction: a retrospective case series
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Background: Fabry disease (FD) is an X-linked lysosomal storage disorder characterized by glycosphingolipid accumulation, resulting in multi-organ dysfunction. Cardiac involvement, known as Fabry cardiomyopathy, may rarely presen... ...