首页 正文

Case Reports Nihon Rinsho Men'eki Gakkai kaishi = Japanese journal of clinical immunology. 2013;36(4):226-32. doi: 10.2177/jsci.36.226

Hemophagocyctic lymphohistiocytosis developed in a Japanese boy with Chédiak-Higashi syndrome

一日本Chediak-Higashi综合征患儿并发噬血细胞淋巴组织细胞增生症 翻译改进

Article in English, Japanese

Takako Miyamae  1, Sakurako Izaki, Koichiro Ikuta, Shumpei Yokota, Hisashi Yamanaka

作者单位 +展开

作者单位

  • 1 Institute of Rheumatology, Tokyo Women's Medical University.
  • DOI: 10.2177/jsci.36.226 PMID: 23994801

    摘要 Ai翻译

    Chédiak-Higashi syndrome (CHS) is one of the primary immunodeficiency syndromes accompanied by oculocutaneous albinism. It is characterized by existence of giant granule of neutrophils, and development of symptoms of hemophagocytic lymphohistiocytosis. CHS is a rare disorder and recognition of the disease is indispensable for its diagnosis. In our case, a four-month-old boy, virus-associated hemophagocytic syndrome (VAHS) was suspected from generation of ... ...点击完成人机验证后继续浏览
    Copyright © Nihon Rinsho Men'eki Gakkai kaishi = Japanese journal of clinical immunology. 中文内容为AI机器翻译,仅供参考!

    相关内容

    全文链接
    引文链接
    复制
    已复制!
    推荐内容
    Hemophagocyctic lymphohistiocytosis developed in a Japanese boy with Chédiak-Higashi syndrome